A novel mutation in the OAR domain of the ARX gene

نویسندگان

  • Alejandra Tapie
  • Natalia Pi‐Denis
  • Jorge Souto
  • Alejandra Vomero
  • Gabriel Peluffo
  • María Boidi
  • Martín Ciganda
  • Nicolás Curbelo
  • Victor Raggio
  • Leda Roche
  • Lucía Pastro
چکیده

Mutations in ARX gene should be considered in patients with mental disability or/and epilepsy. It is an X-linked gene that has pleiotropic effects. Here, we report the case of a boy diagnosed with Ohtahara syndrome. We performed the molecular analysis of the gene and identified a new missense mutation.

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عنوان ژورنال:

دوره 5  شماره 

صفحات  -

تاریخ انتشار 2017